Annotation Detail

Information
Associated Genes
GNPTAB
Associated Variants
GNPTAB p.Arg46= (p.R46=) ( ENST00000549165.1, ENST00000299314.12, ENST00000549940.5, ENST00000392919.4 )
GNPTAB p.Arg46= (p.R46=) ( ENST00000299314.12, ENST00000392919.4, ENST00000549165.1, ENST00000549940.5 )
Associated Disease
Mucolipidosis type II
Source Database
ClinVar
Description
NM_024312.5(GNPTAB):c.136C>A (p.Arg46=) AND Mucolipidosis type II
ClinVar Allele ID
237191
ClinVar RefSeq Alternation Syntax
NM_024312.5:c.136C>A
Clinical Significance Description
Likely benign
Clinical Significance Last Update
2017-04-28
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000379680
ClinVar Disease
Mucolipidosis type II
Observed Origin Sample
germline
Drugs