Annotation Detail

Information
Associated Genes
HNF1A
Associated Variants
HNF1A p.Leu459= (p.L459=) ( ENST00000541395.5, ENST00000544413.2, ENST00000400024.6, ENST00000257555.11 )
HNF1A p.Leu459= (p.L459=) ( ENST00000257555.11, ENST00000400024.6, ENST00000541395.5, ENST00000544413.2 )
Associated Disease
maturity-onset diabetes of the young type 3
Source Database
ClinVar
Description
NM_000545.8(HNF1A):c.1375C>T (p.Leu459=) AND Maturity-onset diabetes of the young type 3
ClinVar Allele ID
134675
ClinVar RefSeq Alternation Syntax
NM_000545.8:c.1375C>T
ClinVar RefSeq Alternation Syntax
NM_001306179.2:c.1375C>T
Clinical Significance Description
Benign
Clinical Significance Last Update
2021-08-10
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000373115
ClinVar Disease
Maturity-onset diabetes of the young type 3
Observed Origin Sample
germline
Drugs