Annotation Detail

Information
Associated Genes
HNF4A
Associated Variants
HNF4A c.116-5C>T ( ENST00000316099.10, ENST00000316673.9, ENST00000415691.2, ENST00000443598.6, ENST00000457232.5, ENST00000609795.5 )
HNF4A c.116-5C>T ( ENST00000316099.10, ENST00000316673.9, ENST00000415691.2, ENST00000443598.6, ENST00000457232.5, ENST00000609795.5 )
Associated Disease
Maturity onset diabetes mellitus in young
Source Database
ClinVar
Description
NM_175914.5(HNF4A):c.50-5C>T AND Maturity onset diabetes mellitus in young
ClinVar Allele ID
134685
ClinVar RefSeq Alternation Syntax
NM_001287183.2:c.41-5C>T
ClinVar RefSeq Alternation Syntax
NM_001287184.2:c.41-5C>T
ClinVar RefSeq Alternation Syntax
NM_001030004.3:c.50-5C>T
ClinVar RefSeq Alternation Syntax
NM_175914.5:c.50-5C>T
ClinVar RefSeq Alternation Syntax
NM_001030003.3:c.50-5C>T
ClinVar RefSeq Alternation Syntax
NM_001287182.2:c.41-5C>T
ClinVar RefSeq Alternation Syntax
NM_000457.6:c.116-5C>T
ClinVar RefSeq Alternation Syntax
NM_178850.3:c.116-5C>T
ClinVar RefSeq Alternation Syntax
NM_001258355.2:c.95-5C>T
ClinVar RefSeq Alternation Syntax
NM_178849.3:c.116-5C>T
Clinical Significance Description
Benign/Likely benign
Clinical Significance Last Update
2016-06-14
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000361090
ClinVar Disease
Maturity onset diabetes mellitus in young
Observed Origin Sample
germline
Drugs