Annotation Detail

Information
Associated Genes
GHSR
Associated Variants
GHSR p.Arg159= (p.R159=) ( ENST00000241256.3, ENST00000427970.1 )
GHSR p.Arg159= (p.R159=) ( ENST00000241256.3, ENST00000427970.1 )
Associated Disease
Short stature due to growth hormone secretagogue receptor deficiency
Source Database
ClinVar
Description
NM_198407.2(GHSR):c.477G>A (p.Arg159=) AND Short stature due to growth hormone secretagogue receptor deficiency
ClinVar Allele ID
251009
ClinVar RefSeq Alternation Syntax
NM_198407.2:c.477G>A
ClinVar RefSeq Alternation Syntax
NM_004122.2:c.477G>A
Clinical Significance Description
Benign
Clinical Significance Last Update
2021-08-10
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000347022
ClinVar Disease
Short stature due to growth hormone secretagogue receptor deficiency
Observed Origin Sample
germline
Drugs