Annotation Detail

Information
Associated Genes
LDLR
Associated Variants
LDLR c.*666T>C ( ENST00000252444.10, ENST00000558518.6, ENST00000560467.2 )
LDLR c.*666T>C ( ENST00000252444.10, ENST00000558518.6, ENST00000560467.2 )
Associated Disease
Hypercholesterolemia, familial, 1
Source Database
ClinVar
Description
NM_000527.5(LDLR):c.*666T>C AND Hypercholesterolemia, familial, 1
ClinVar Allele ID
348008
ClinVar RefSeq Alternation Syntax
NM_000527.5:c.*666T>C
ClinVar RefSeq Alternation Syntax
NM_001195803.2:c.*666T>C
ClinVar RefSeq Alternation Syntax
NM_001195799.2:c.*666T>C
ClinVar RefSeq Alternation Syntax
NM_001195798.2:c.*666T>C
ClinVar RefSeq Alternation Syntax
NM_001195800.2:c.*666T>C
Clinical Significance Description
Benign/Likely benign
Clinical Significance Last Update
2018-01-13
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000346475
ClinVar Disease
Hypercholesterolemia, familial, 1
Observed Origin Sample
germline
Drugs