Annotation Detail

Information
Associated Genes
ERCC2
Associated Variants
ERCC2 p.Lys751Gln (p.K751Q) ( ENST00000391944.8, ENST00000391945.10, ENST00000684407.1 )
ERCC2 p.Lys751Gln (p.K751Q) ( ENST00000391944.8, ENST00000391945.10, ENST00000684407.1 )
Associated Disease
Xeroderma pigmentosum, group D
Source Database
ClinVar
Description
NM_000400.4(ERCC2):c.2251A>C (p.Lys751Gln) AND Xeroderma pigmentosum, group D
ClinVar Allele ID
137844
ClinVar RefSeq Alternation Syntax
NM_000400.4:c.2251A>C
Clinical Significance Description
Benign
Clinical Significance Last Update
2021-07-30
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000282755
ClinVar Disease
Xeroderma pigmentosum, group D
Observed Origin Sample
germline
Drugs