Annotation Detail

Information
Associated Genes
NFKBIA
Associated Variants
NFKBIA c.*126G>A ( ENST00000557140.5, ENST00000697961.1, ENST00000557389.1, ENST00000216797.10 )
NFKBIA c.*126G>A ( ENST00000216797.10, ENST00000557140.5, ENST00000557389.1, ENST00000697961.1 )
Associated Disease
ectodermal dysplasia and immunodeficiency 2
Source Database
ClinVar
Description
NM_020529.3(NFKBIA):c.*126G>A AND Ectodermal dysplasia and immunodeficiency 2
ClinVar Allele ID
337761
ClinVar RefSeq Alternation Syntax
NM_020529.3:c.*126G>A
Clinical Significance Description
Benign
Clinical Significance Last Update
2020-11-25
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000260426
ClinVar Disease
Ectodermal dysplasia and immunodeficiency 2
Observed Origin Sample
germline
Drugs