Annotation Detail

Information
Associated Genes
PKP2
Associated Variants
PKP2 p.His733AlafsTer8 (p.H733Afs*8) ( ENST00000340811.9, ENST00000070846.11, ENST00000549461.3, ENST00000700559.2, ENST00000700558.2 )
PKP2 p.His733AlafsTer8 (p.H733Afs*8) ( ENST00000070846.11, ENST00000340811.9, ENST00000549461.3, ENST00000700558.2, ENST00000700559.2 )
Source Database
ClinVar
Description
NM_001005242.3(PKP2):c.2065_2070delinsG (p.His689fs) AND Cardiovascular phenotype
ClinVar Allele ID
54230
ClinVar RefSeq Alternation Syntax
NM_004572.4:c.2197_2202delinsG
ClinVar RefSeq Alternation Syntax
NM_001005242.3:c.2065_2070delinsG
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2021-10-25
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000247451
Observed Origin Sample
germline
Drugs