Annotation Detail

Information
Associated Genes
PKP2
Associated Variants
PKP2 p.Arg79Ter (p.R79*) ( ENST00000340811.9, ENST00000700559.2, ENST00000070846.11, ENST00000700564.2, ENST00000700563.2 )
PKP2 p.Arg79Ter (p.R79*) ( ENST00000070846.11, ENST00000340811.9, ENST00000700559.2, ENST00000700563.2, ENST00000700564.2 )
Source Database
ClinVar
Description
NM_001005242.3(PKP2):c.235C>T (p.Arg79Ter) AND Cardiovascular phenotype
ClinVar Allele ID
21793
ClinVar RefSeq Alternation Syntax
NM_001005242.3:c.235C>T
ClinVar RefSeq Alternation Syntax
NM_004572.4:c.235C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2021-12-17
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000246785
Observed Origin Sample
germline
Drugs