Annotation Detail

Information
Associated Genes
SMO
Associated Variants
SMO p.Leu412Phe (p.L412F) ( ENST00000249373.8 )
SMO p.Leu412Phe (p.L412F) ( ENST00000249373.8 )
Associated Disease
Curry-Jones syndrome
Source Database
ClinVar
Description
NM_005631.5(SMO):c.1234C>T (p.Leu412Phe) AND Curry-Jones syndrome
ClinVar Allele ID
245206
ClinVar RefSeq Alternation Syntax
NM_005631.5:c.1234C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2019-03-22
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000236033
ClinVar Disease
Curry-Jones syndrome
Observed Origin Sample
somatic
Pubmed
3144990
Pubmed
16531740
Pubmed
18798318
Pubmed
27236920
Pubmed
7606318
Drugs