Annotation Detail

Information
Associated Genes
PTEN
Associated Variants
PTEN p.Arg173Cys (p.R173C) ( ENST00000472832.3, ENST00000371953.8, ENST00000688308.1, ENST00000700021.1, ENST00000700029.2, ENST00000713839.1 )
PTEN p.Arg173Cys (p.R173C) ( ENST00000371953.8, ENST00000472832.3, ENST00000688308.1, ENST00000700021.1, ENST00000700029.2, ENST00000713839.1 )
Associated Disease
Hereditary cancer-predisposing syndrome
Source Database
ClinVar
Description
NM_000314.8(PTEN):c.517C>T (p.Arg173Cys) AND Hereditary cancer-predisposing syndrome
ClinVar Allele ID
187363
ClinVar RefSeq Alternation Syntax
NM_001304718.2:c.-75C>T
ClinVar RefSeq Alternation Syntax
NM_001304717.5:c.1036C>T
ClinVar RefSeq Alternation Syntax
NM_000314.8:c.517C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2022-06-09
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000218276
ClinVar Disease
Hereditary cancer-predisposing syndrome
Observed Origin Sample
germline
Drugs