Annotation Detail

Information
Associated Genes
TMEM67
Associated Variants
TMEM67 c.2322+5delG ( ENST00000409623.8, ENST00000452276.6, ENST00000453321.8, ENST00000453906.6, ENST00000519845.5, ENST00000520680.2, ENST00000521517.6, ENST00000682036.1, ENST00000683362.1, ENST00000684064.1, ENST00000684343.1 )
TMEM67 c.2322+5delG ( ENST00000409623.8, ENST00000452276.6, ENST00000453321.8, ENST00000453906.6, ENST00000519845.5, ENST00000520680.2, ENST00000521517.6, ENST00000682036.1, ENST00000683362.1, ENST00000684064.1, ENST00000684343.1 )
Associated Disease
Joubert syndrome 6
Source Database
ClinVar
Description
NM_153704.6(TMEM67):c.2322+5del AND Joubert syndrome 6
ClinVar Allele ID
214289
ClinVar RefSeq Alternation Syntax
NM_153704.6:c.2322+5del
ClinVar RefSeq Alternation Syntax
NM_001142301.1:c.2079+5del
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2015-02-23
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000201630
ClinVar Disease
Joubert syndrome 6
Observed Origin Sample
unknown
Drugs