Annotation Detail

Information
Associated Genes
PIK3CA
Associated Variants
PIK3CA p.Met1043Ile (p.M1043I) ( ENST00000643187.1, ENST00000263967.4 )
PIK3CA p.Met1043Ile (p.M1043I) ( ENST00000263967.4, ENST00000643187.1 )
Associated Disease
PIK3CA related overgrowth syndrome
Source Database
ClinVar
Description
NM_006218.4(PIK3CA):c.3129G>T (p.Met1043Ile) AND PIK3CA related overgrowth syndrome
ClinVar Allele ID
213942
ClinVar RefSeq Alternation Syntax
NM_006218.4:c.3129G>T
Clinical Significance Description
Pathogenic
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000201236
ClinVar Disease
PIK3CA related overgrowth syndrome
Observed Origin Sample
de novo
Observed Origin Sample
somatic
Drugs