Annotation Detail

Information
Associated Genes
ATP7A
Associated Variants
ATP7A p.Tyr594Ter (p.Y594*) ( ENST00000341514.11, ENST00000343533.10, ENST00000685264.1, ENST00000686033.1, ENST00000686133.1, ENST00000686480.1, ENST00000686543.1, ENST00000686688.1, ENST00000687086.1, ENST00000689649.1, ENST00000689767.1, ENST00000692908.1, ENST00000693398.1, ENST00000644362.1 )
ATP7A p.Tyr594Ter (p.Y594*) ( ENST00000341514.11, ENST00000343533.10, ENST00000685264.1, ENST00000686033.1, ENST00000686133.1, ENST00000686480.1, ENST00000686543.1, ENST00000686688.1, ENST00000687086.1, ENST00000689649.1, ENST00000689767.1, ENST00000692908.1, ENST00000693398.1, ENST00000644362.1 )
Associated Disease
Menkes kinky-hair syndrome
Source Database
ClinVar
Description
NM_000052.7(ATP7A):c.1782C>G (p.Tyr594Ter) AND Menkes kinky-hair syndrome
ClinVar Allele ID
209224
ClinVar RefSeq Alternation Syntax
NM_000052.7:c.1782C>G
ClinVar RefSeq Alternation Syntax
NM_001282224.2:c.1782C>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2018-05-02
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000192830
ClinVar Disease
Menkes kinky-hair syndrome
Observed Origin Sample
germline
Drugs