Annotation Detail

Information
Associated Genes
WFS1
Associated Variants
WFS1 p.Cys755Arg (p.C755R) ( ENST00000226760.5, ENST00000503569.5, ENST00000506362.2, ENST00000673991.1, ENST00000682275.1, ENST00000684087.1 )
WFS1 p.Cys755Arg (p.C755R) ( ENST00000226760.5, ENST00000503569.5, ENST00000506362.2, ENST00000673991.1, ENST00000682275.1, ENST00000684087.1 )
Associated Disease
Wolfram syndrome 1
Source Database
ClinVar
Description
NM_006005.3(WFS1):c.2263T>C (p.Cys755Arg) AND Wolfram syndrome 1
ClinVar Allele ID
205739
ClinVar RefSeq Alternation Syntax
NM_001145853.1:c.2263T>C
ClinVar RefSeq Alternation Syntax
NM_006005.3:c.2263T>C
Clinical Significance Description
Likely pathogenic/Likely risk allele
Clinical Significance Last Update
2013-10-22
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000191145
ClinVar Disease
Wolfram syndrome 1
Observed Origin Sample
maternal
Observed Origin Sample
unknown
Drugs