Annotation Detail

Information
Associated Genes
NF1
Associated Variants
NF1 c.1642-8A>G ( ENST00000696138.1, ENST00000358273.9, ENST00000356175.7, ENST00000691014.1, ENST00000431387.8 )
NF1 c.1642-8A>G ( ENST00000356175.7, ENST00000358273.9, ENST00000431387.8, ENST00000691014.1, ENST00000696138.1 )
Associated Disease
Neurofibromatosis, type 1
Source Database
ClinVar
Description
NM_001042492.3(NF1):c.1642-8A>G AND Neurofibromatosis, type 1
ClinVar Allele ID
15391
ClinVar RefSeq Alternation Syntax
NM_001042492.3:c.1642-8A>G
ClinVar RefSeq Alternation Syntax
NM_000267.3:c.1642-8A>G
ClinVar RefSeq Alternation Syntax
NM_001128147.3:c.1642-8A>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2022-08-17
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000190422
ClinVar Disease
Neurofibromatosis, type 1
Observed Origin Sample
germline
Pubmed
9639526
Pubmed
9180088
Drugs