Annotation Detail

Information
Associated Genes
RNF216
Associated Variants
RNF216 p.Tyr539Cys (p.Y539C) ( ENST00000389902.8, ENST00000425013.6 )
RNF216 p.Tyr539Cys (p.Y539C) ( ENST00000389902.8, ENST00000425013.6 )
Associated Disease
Cerebellar ataxia-hypogonadism syndrome
Source Database
ClinVar
Description
NM_207111.4(RNF216):c.1616A>G (p.Tyr539Cys) AND Cerebellar ataxia-hypogonadism syndrome
ClinVar Allele ID
196434
ClinVar RefSeq Alternation Syntax
NM_207111.4:c.1616A>G
ClinVar RefSeq Alternation Syntax
NM_207116.3:c.1445A>G
Clinical Significance Description
Uncertain significance
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000180795
ClinVar Disease
Cerebellar ataxia-hypogonadism syndrome
Observed Origin Sample
germline
Pubmed
25841028
Drugs