Annotation Detail

Information
Associated Genes
RNF216
Associated Variants
RNF216 p.Gly456Glu (p.G456E) ( ENST00000389902.8, ENST00000425013.6 )
RNF216 p.Gly456Glu (p.G456E) ( ENST00000389902.8, ENST00000425013.6 )
Associated Disease
Cerebellar ataxia-hypogonadism syndrome
Source Database
ClinVar
Description
NM_207111.4(RNF216):c.1367G>A (p.Gly456Glu) AND Cerebellar ataxia-hypogonadism syndrome
ClinVar Allele ID
196432
ClinVar RefSeq Alternation Syntax
NM_207111.4:c.1367G>A
ClinVar RefSeq Alternation Syntax
NM_207116.3:c.1196G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2015-04-28
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000180793
ClinVar Disease
Cerebellar ataxia-hypogonadism syndrome
Observed Origin Sample
germline
Pubmed
25841028
Drugs