Annotation Detail

Information
Associated Genes
XPC
Associated Variants
XPC p.Tyr559Ter (p.Y559*) ( ENST00000285021.12 )
XPC p.Tyr559Ter (p.Y559*) ( ENST00000285021.12 )
Associated Disease
Xeroderma pigmentosum, group C
Source Database
ClinVar
Description
NM_004628.5(XPC):c.1677C>A (p.Tyr559Ter) AND Xeroderma pigmentosum, group C
ClinVar Allele ID
187978
ClinVar RefSeq Alternation Syntax
NR_148950.2:n.1710C>A
ClinVar RefSeq Alternation Syntax
NM_001354729.2:c.1659C>A
ClinVar RefSeq Alternation Syntax
NM_004628.5:c.1677C>A
ClinVar RefSeq Alternation Syntax
NM_001354727.2:c.1677C>A
ClinVar RefSeq Alternation Syntax
NM_001354730.2:c.1626+51C>A
ClinVar RefSeq Alternation Syntax
NM_001354726.2:c.1098C>A
ClinVar RefSeq Alternation Syntax
NR_148951.2:n.1586C>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2017-08-25
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000170432
ClinVar Disease
Xeroderma pigmentosum, group C
Observed Origin Sample
germline
Observed Origin Sample
unknown
Drugs