Annotation Detail

Information
Associated Genes
XPC
Associated Variants
XPC p.Asn754LysfsTer13 (p.N754Kfs*13) ( ENST00000285021.12 )
XPC p.Asn754LysfsTer13 (p.N754Kfs*13) ( ENST00000285021.12 )
Associated Disease
Xeroderma pigmentosum, group C
Source Database
ClinVar
Description
NM_004628.5(XPC):c.2262del (p.Asn754fs) AND Xeroderma pigmentosum, group C
ClinVar Allele ID
187974
ClinVar RefSeq Alternation Syntax
NM_001354727.2:c.2256del
ClinVar RefSeq Alternation Syntax
NM_004628.5:c.2262del
ClinVar RefSeq Alternation Syntax
NR_148950.2:n.2134del
ClinVar RefSeq Alternation Syntax
NM_001354730.2:c.2016del
ClinVar RefSeq Alternation Syntax
NM_001354729.2:c.2244del
ClinVar RefSeq Alternation Syntax
NM_001354726.2:c.1683del
ClinVar RefSeq Alternation Syntax
NR_148951.2:n.2010del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2011-01-27
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000170429
ClinVar Disease
Xeroderma pigmentosum, group C
Observed Origin Sample
germline
Drugs