Annotation Detail

Information
Associated Genes
PTEN
Associated Variants
PTEN p.Ile253LysfsTer2 (p.I253Kfs*2) ( ENST00000700021.1, ENST00000472832.3, ENST00000713839.1, ENST00000371953.8, ENST00000700029.2, ENST00000688308.1 )
PTEN p.Ile253LysfsTer2 (p.I253Kfs*2) ( ENST00000371953.8, ENST00000472832.3, ENST00000688308.1, ENST00000700021.1, ENST00000700029.2, ENST00000713839.1 )
Associated Disease
Hereditary cancer-predisposing syndrome
Source Database
ClinVar
Description
NM_000314.8(PTEN):c.758_761del (p.Ile253fs) AND Hereditary cancer-predisposing syndrome
ClinVar Allele ID
187374
ClinVar RefSeq Alternation Syntax
NM_001304717.5:c.1277_1280del
ClinVar RefSeq Alternation Syntax
NM_001304718.2:c.167_170del
ClinVar RefSeq Alternation Syntax
NM_000314.8:c.758_761del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2014-03-25
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000169844
ClinVar Disease
Hereditary cancer-predisposing syndrome
Observed Origin Sample
germline
Drugs