Annotation Detail

Information
Associated Genes
PPOX
Associated Variants
PPOX p.Leu67Ter (p.L67*) ( ENST00000352210.9, ENST00000462866.5, ENST00000544598.5, ENST00000367999.9, ENST00000535223.5 )
PPOX p.Leu67Ter (p.L67*) ( ENST00000352210.9, ENST00000367999.9, ENST00000462866.5, ENST00000535223.5, ENST00000544598.5 )
Associated Disease
variegate porphyria
Source Database
ClinVar
Description
NM_001122764.3(PPOX):c.199del (p.Ala66_Leu67insTer) AND Variegate porphyria
ClinVar Allele ID
187104
ClinVar RefSeq Alternation Syntax
NM_001122764.3:c.199del
ClinVar RefSeq Alternation Syntax
NM_001365399.1:c.199del
ClinVar RefSeq Alternation Syntax
NM_001350128.2:c.199del
ClinVar RefSeq Alternation Syntax
NM_001365401.1:c.-172del
ClinVar RefSeq Alternation Syntax
NM_001365398.1:c.199del
ClinVar RefSeq Alternation Syntax
NM_001350130.2:c.-320del
ClinVar RefSeq Alternation Syntax
NM_001365400.1:c.-113del
ClinVar RefSeq Alternation Syntax
NM_001350129.2:c.-229del
ClinVar RefSeq Alternation Syntax
NM_001350131.2:c.-206del
ClinVar RefSeq Alternation Syntax
NM_000309.5:c.199del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2014-03-24
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000169672
ClinVar Disease
Variegate porphyria
Observed Origin Sample
germline
Drugs