Annotation Detail

Information
Associated Genes
HBB LOC106099062 LOC107133510
Associated Variants
HBB p.Gly84AlafsTer6 (p.G84Afs*6) ( ENST00000647020.1, ENST00000335295.4, ENST00000485743.1 )
HBB p.Gly84AlafsTer6 (p.G84Afs*6) ( ENST00000335295.4, ENST00000485743.1, ENST00000647020.1 )
Associated Disease
beta thalassemia
Source Database
ClinVar
Description
NM_000518.5(HBB):c.251del (p.Gly84fs) AND beta Thalassemia
ClinVar Allele ID
44970
ClinVar RefSeq Alternation Syntax
NM_000518.5:c.251del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2017-05-24
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000169623
ClinVar Disease
beta Thalassemia
Observed Origin Sample
germline
Observed Origin Sample
unknown
Drugs