Annotation Detail

Information
Associated Genes
NF1
Associated Variants
NF1 p.Glu595AsnfsTer14 (p.E595Nfs*14) ( ENST00000696138.1, ENST00000358273.9, ENST00000691014.1, ENST00000356175.7 )
NF1 p.Glu595AsnfsTer14 (p.E595Nfs*14) ( ENST00000356175.7, ENST00000358273.9, ENST00000691014.1, ENST00000696138.1 )
Associated Disease
Neurofibromatosis, type 1
Source Database
ClinVar
Description
NM_001042492.3(NF1):c.1783_1784del (p.Glu595fs) AND Neurofibromatosis, type 1
ClinVar Allele ID
186246
ClinVar RefSeq Alternation Syntax
NM_000267.3:c.1783_1784del
ClinVar RefSeq Alternation Syntax
NM_001042492.3:c.1783_1784del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-11-17
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000167922
ClinVar Disease
Neurofibromatosis, type 1
Observed Origin Sample
germline
Drugs