Annotation Detail

Information
Associated Genes
MTHFR
Associated Variants
MTHFR c.1875+1G>T ( ENST00000376590.9, ENST00000641407.1, ENST00000376592.6, ENST00000376585.6, ENST00000376583.7, ENST00000423400.7, ENST00000641820.1 )
MTHFR c.1875+1G>T ( ENST00000376583.7, ENST00000376585.6, ENST00000376590.9, ENST00000376592.6, ENST00000423400.7, ENST00000641407.1, ENST00000641820.1 )
Associated Disease
Homocystinuria due to methylene tetrahydrofolate reductase deficiency
Source Database
ClinVar
Description
NM_005957.5(MTHFR):c.1752+1G>T AND Homocystinuria due to methylene tetrahydrofolate reductase deficiency
ClinVar Allele ID
185763
ClinVar RefSeq Alternation Syntax
NM_001330358.2:c.1875+1G>T
ClinVar RefSeq Alternation Syntax
NM_001410750.1:c.1872+1G>T
ClinVar RefSeq Alternation Syntax
NM_005957.5:c.1752+1G>T
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2023-06-20
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000167620
ClinVar Disease
Homocystinuria due to methylene tetrahydrofolate reductase deficiency
Observed Origin Sample
germline
Drugs