Annotation Detail

Information
Associated Genes
MTHFR
Associated Variants
MTHFR p.Ile266Leu (p.I266L) ( ENST00000376590.9, ENST00000376592.6, ENST00000641407.1, ENST00000376585.6, ENST00000423400.7, ENST00000641820.1, ENST00000376583.7 )
MTHFR p.Ile266Leu (p.I266L) ( ENST00000376583.7, ENST00000376585.6, ENST00000376590.9, ENST00000376592.6, ENST00000423400.7, ENST00000641407.1, ENST00000641820.1 )
Associated Disease
Homocystinuria due to methylene tetrahydrofolate reductase deficiency
Source Database
ClinVar
Description
NM_005957.5(MTHFR):c.673A>C (p.Ile225Leu) AND Homocystinuria due to methylene tetrahydrofolate reductase deficiency
ClinVar Allele ID
185784
ClinVar RefSeq Alternation Syntax
NM_005957.5:c.673A>C
ClinVar RefSeq Alternation Syntax
NM_001330358.2:c.796A>C
Clinical Significance Description
Pathogenic
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000167599
ClinVar Disease
Homocystinuria due to methylene tetrahydrofolate reductase deficiency
Observed Origin Sample
germline
Drugs