Annotation Detail

Information
Associated Genes
MTHFR
Associated Variants
MTHFR p.Trp100Ser (p.W100S) ( ENST00000376585.6, ENST00000376583.7, ENST00000423400.7, ENST00000376590.9, ENST00000376592.6, ENST00000641407.1 )
MTHFR p.Trp100Ser (p.W100S) ( ENST00000376583.7, ENST00000376585.6, ENST00000376590.9, ENST00000376592.6, ENST00000423400.7, ENST00000641407.1 )
Associated Disease
Homocystinuria due to methylene tetrahydrofolate reductase deficiency
Source Database
ClinVar
Description
NM_005957.5(MTHFR):c.176G>C (p.Trp59Ser) AND Homocystinuria due to methylene tetrahydrofolate reductase deficiency
ClinVar Allele ID
185795
ClinVar RefSeq Alternation Syntax
NM_005957.5:c.176G>C
ClinVar RefSeq Alternation Syntax
NM_001330358.2:c.299G>C
Clinical Significance Description
Pathogenic
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000167588
ClinVar Disease
Homocystinuria due to methylene tetrahydrofolate reductase deficiency
Observed Origin Sample
germline
Drugs