Annotation Detail

Information
Associated Genes
BARD1
Associated Variants
BARD1 p.Ser400ValfsTer8 (p.S400Vfs*8) ( ENST00000260947.9, ENST00000421162.2, ENST00000613374.5, ENST00000613706.5, ENST00000617164.5, ENST00000619009.5, ENST00000620057.4 )
BARD1 p.Ser400ValfsTer8 (p.S400Vfs*8) ( ENST00000260947.9, ENST00000421162.2, ENST00000613374.5, ENST00000613706.5, ENST00000617164.5, ENST00000619009.5, ENST00000620057.4 )
Associated Disease
Hereditary cancer-predisposing syndrome
Source Database
ClinVar
Description
NM_000465.4(BARD1):c.1198del (p.Ser400fs) AND Hereditary cancer-predisposing syndrome
ClinVar Allele ID
181808
ClinVar RefSeq Alternation Syntax
NR_104212.2:n.1163del
ClinVar RefSeq Alternation Syntax
NM_001282545.2:c.215+16385del
ClinVar RefSeq Alternation Syntax
NM_000465.4:c.1198del
ClinVar RefSeq Alternation Syntax
NM_001282543.2:c.1141del
ClinVar RefSeq Alternation Syntax
NM_001282548.2:c.159-28121del
ClinVar RefSeq Alternation Syntax
NR_104215.2:n.1106del
ClinVar RefSeq Alternation Syntax
NM_001282549.2:c.364+11621del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2014-12-17
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000167393
ClinVar Disease
Hereditary cancer-predisposing syndrome
Observed Origin Sample
germline
Drugs