Annotation Detail

Information
Associated Genes
NF1
Associated Variants
NF1 p.Gln209Ter (p.Q209*) ( ENST00000490416.2, ENST00000487476.5, ENST00000696138.1, ENST00000356175.7, ENST00000358273.9, ENST00000431387.8, ENST00000691014.1 )
NF1 p.Gln209Ter (p.Q209*) ( ENST00000356175.7, ENST00000358273.9, ENST00000431387.8, ENST00000487476.5, ENST00000490416.2, ENST00000691014.1, ENST00000696138.1 )
Associated Disease
Hereditary cancer-predisposing syndrome
Source Database
ClinVar
Description
NM_001042492.3(NF1):c.625C>T (p.Gln209Ter) AND Hereditary cancer-predisposing syndrome
ClinVar Allele ID
184516
ClinVar RefSeq Alternation Syntax
NM_000267.3:c.625C>T
ClinVar RefSeq Alternation Syntax
NM_001128147.3:c.625C>T
ClinVar RefSeq Alternation Syntax
NM_001042492.3:c.625C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2014-11-04
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000166757
ClinVar Disease
Hereditary cancer-predisposing syndrome
Observed Origin Sample
germline
Drugs