Annotation Detail

Information
Associated Genes
PTEN
Associated Variants
PTEN p.Arg159Gly (p.R159G) ( ENST00000371953.8, ENST00000472832.3, ENST00000688308.1, ENST00000700021.1, ENST00000700029.2, ENST00000713839.1 )
PTEN p.Arg159Gly (p.R159G) ( ENST00000371953.8, ENST00000472832.3, ENST00000688308.1, ENST00000700021.1, ENST00000700029.2, ENST00000713839.1 )
Associated Disease
Hereditary cancer-predisposing syndrome
Source Database
ClinVar
Description
NM_000314.8(PTEN):c.475A>G (p.Arg159Gly) AND Hereditary cancer-predisposing syndrome
ClinVar Allele ID
183032
ClinVar RefSeq Alternation Syntax
NM_001304717.5:c.994A>G
ClinVar RefSeq Alternation Syntax
NM_000314.8:c.475A>G
ClinVar RefSeq Alternation Syntax
NM_001304718.2:c.-276A>G
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2024-02-05
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000165624
ClinVar Disease
Hereditary cancer-predisposing syndrome
Observed Origin Sample
germline
Drugs