Annotation Detail

Information
Associated Genes
NF1
Associated Variants
NF1 p.Asp2465IlefsTer24 (p.D2465Ifs*24) ( ENST00000684826.1, ENST00000696138.1, ENST00000358273.9, ENST00000693617.1, ENST00000687027.1, ENST00000356175.7, ENST00000691014.1 )
NF1 p.Asp2465IlefsTer24 (p.D2465Ifs*24) ( ENST00000356175.7, ENST00000358273.9, ENST00000684826.1, ENST00000687027.1, ENST00000691014.1, ENST00000693617.1, ENST00000696138.1 )
Associated Disease
Hereditary cancer-predisposing syndrome
Source Database
ClinVar
Description
NM_001042492.3(NF1):c.7392del (p.Asp2465fs) AND Hereditary cancer-predisposing syndrome
ClinVar Allele ID
184751
ClinVar RefSeq Alternation Syntax
NM_000267.3:c.7329del
ClinVar RefSeq Alternation Syntax
NM_001042492.3:c.7392del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2014-07-03
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000164876
ClinVar Disease
Hereditary cancer-predisposing syndrome
Observed Origin Sample
germline
Drugs