Annotation Detail

Information
Associated Genes
MYH7
Associated Variants
MYH7 p.Tyr386Cys (p.Y386C) ( ENST00000713769.1, ENST00000355349.4, ENST00000713768.1 )
MYH7 p.Tyr386Cys (p.Y386C) ( ENST00000355349.4, ENST00000713768.1, ENST00000713769.1 )
Associated Disease
left ventricular noncompaction hypertrophic cardiomyopathy restrictive cardiomyopathy
Source Database
ClinVar
Description
NM_000257.4(MYH7):c.1157A>G (p.Tyr386Cys) AND multiple conditions
ClinVar Allele ID
175645
ClinVar RefSeq Alternation Syntax
NM_000257.4:c.1157A>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2013-08-23
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000151296
ClinVar Disease
Restrictive cardiomyopathy
ClinVar Disease
Left ventricular noncompaction
ClinVar Disease
Hypertrophic cardiomyopathy
Observed Origin Sample
germline
Drugs