Annotation Detail

Information
Associated Genes
KRAS
Associated Variants
KRAS c.*20T>A ( ENST00000256078.10, ENST00000688940.1, ENST00000557334.6, ENST00000685328.1, ENST00000692768.1, ENST00000693229.1, ENST00000311936.8 )
KRAS c.*20T>A ( ENST00000256078.10, ENST00000311936.8, ENST00000557334.6, ENST00000685328.1, ENST00000688940.1, ENST00000692768.1, ENST00000693229.1 )
Associated Disease
Noonan syndrome Cardio-facio-cutaneous syndrome
Source Database
ClinVar
Description
NM_004985.5(KRAS):c.466T>A (p.Phe156Ile) AND multiple conditions
ClinVar Allele ID
175711
ClinVar RefSeq Alternation Syntax
NM_004985.5:c.466T>A
ClinVar RefSeq Alternation Syntax
NM_001369786.1:c.*20T>A
ClinVar RefSeq Alternation Syntax
NM_033360.4:c.*20T>A
ClinVar RefSeq Alternation Syntax
NM_001369787.1:c.466T>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2018-02-15
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000150884
ClinVar Disease
Noonan syndrome
ClinVar Disease
Cardio-facio-cutaneous syndrome
Observed Origin Sample
germline
Drugs