Annotation Detail

Information
Associated Genes
BRAF
Associated Variants
BRAF p.Asp678Glu (p.D678E) ( ENST00000288602.11, ENST00000496384.7, ENST00000644969.2, ENST00000646891.2 )
BRAF p.Asp678Glu (p.D678E) ( ENST00000288602.11, ENST00000496384.7, ENST00000644969.2, ENST00000646891.2 )
Associated Disease
Cardio-facio-cutaneous syndrome
Source Database
ClinVar
Description
NM_001374258.1(BRAF):c.2034T>G (p.Asp678Glu) AND Cardio-facio-cutaneous syndrome
ClinVar Allele ID
174176
ClinVar RefSeq Alternation Syntax
NM_001374258.1:c.2034T>G
ClinVar RefSeq Alternation Syntax
NM_001378469.1:c.1848T>G
ClinVar RefSeq Alternation Syntax
NM_001378468.1:c.1914T>G
ClinVar RefSeq Alternation Syntax
NM_004333.6:c.1914T>G
ClinVar RefSeq Alternation Syntax
NM_001378470.1:c.1812T>G
ClinVar RefSeq Alternation Syntax
NM_001374244.1:c.2034T>G
ClinVar RefSeq Alternation Syntax
NM_001378474.1:c.1914T>G
ClinVar RefSeq Alternation Syntax
NM_001378467.1:c.1923T>G
ClinVar RefSeq Alternation Syntax
NM_001378471.1:c.1803T>G
ClinVar RefSeq Alternation Syntax
NM_001378475.1:c.1650T>G
ClinVar RefSeq Alternation Syntax
NM_001354609.2:c.1914T>G
ClinVar RefSeq Alternation Syntax
NM_001378473.1:c.1758T>G
ClinVar RefSeq Alternation Syntax
NM_001378472.1:c.1758T>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2024-03-14
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000150199
ClinVar Disease
Cardio-facio-cutaneous syndrome
Observed Origin Sample
germline
Drugs