Annotation Detail

Information
Associated Genes
PIK3CA
Associated Variants
PIK3CA p.Ser553ThrfsTer7 (p.S553Tfs*7) ( ENST00000263967.4, ENST00000643187.1 )
PIK3CA p.Ser553ThrfsTer7 (p.S553Tfs*7) ( ENST00000263967.4, ENST00000643187.1 )
PIK3CA p.Glu545Ala (p.E545A) ( ENST00000263967.4, ENST00000643187.1 )
PIK3CA p.Glu545Ala (p.E545A) ( ENST00000263967.4, ENST00000643187.1 )
Associated Disease
Cowden syndrome 5
Source Database
ClinVar
Description
NM_006218.3(PIK3CA):c.[1634A>C;1658_1659delGTinsC] AND Cowden syndrome 5
ClinVar Allele ID
28698
ClinVar Allele ID
166223
ClinVar RefSeq Alternation Syntax
NM_006218.4:c.1658_1659delinsC
ClinVar RefSeq Alternation Syntax
NM_006218.4:c.1634A>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2013-01-10
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000144511
ClinVar Disease
Cowden syndrome 5
Observed Origin Sample
germline
Pubmed
23246288
Drugs