Annotation Detail

Information
Associated Genes
ACTB
Associated Variants
ACTB p.Val103Leu (p.V103L) ( ENST00000432588.6, ENST00000473257.3, ENST00000493945.6, ENST00000642480.2, ENST00000646664.1, ENST00000674681.1, ENST00000675515.1, ENST00000676319.1, ENST00000676397.1 )
ACTB p.Val103Leu (p.V103L) ( ENST00000432588.6, ENST00000473257.3, ENST00000493945.6, ENST00000642480.2, ENST00000646664.1, ENST00000674681.1, ENST00000675515.1, ENST00000676319.1, ENST00000676397.1 )
Associated Disease
Baraitser-Winter syndrome 1
Source Database
ClinVar
Description
NM_001101.5(ACTB):c.307G>C (p.Val103Leu) AND Baraitser-Winter syndrome 1
ClinVar Allele ID
132663
ClinVar RefSeq Alternation Syntax
NM_001101.5:c.307G>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2014-04-15
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000133568
ClinVar Disease
Baraitser-Winter syndrome 1
Observed Origin Sample
germline
Drugs