Annotation Detail

Information
Associated Genes
ABCA4
Associated Variants
ABCA4 p.Asn933Ile (p.N933I) ( ENST00000370225.4, ENST00000649773.1 )
ABCA4 p.Asn933Ile (p.N933I) ( ENST00000370225.4, ENST00000649773.1 )
Associated Disease
Severe early-childhood-onset retinal dystrophy
Source Database
ClinVar
Description
NM_000350.3(ABCA4):c.2798A>T (p.Asn933Ile) AND Severe early-childhood-onset retinal dystrophy
ClinVar Allele ID
152792
ClinVar RefSeq Alternation Syntax
NM_001425324.1:c.2576A>T
ClinVar RefSeq Alternation Syntax
NM_000350.3:c.2798A>T
Clinical Significance Description
Pathogenic
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000132589
ClinVar Disease
Severe early-childhood-onset retinal dystrophy
Observed Origin Sample
not provided
Drugs