Annotation Detail

Information
Associated Genes
MUTYH
Associated Variants
MUTYH p.Arg516Gln (p.R516Q), ENSG00000288208 c.*215G>A ( ENST00000488731.6, ENST00000713751.1, ENST00000412971.6, ENST00000528013.6, ENST00000372104.5, ENST00000355498.6, ENST00000372115.7, ENST00000529984.5, ENST00000354383.10, ENST00000456914.7, ENST00000483127.2, ENST00000672314.2, ENST00000713750.1, ENST00000372110.7, ENST00000710952.2, ENST00000372098.7, ENST00000448481.5, ENST00000529892.6, ENST00000531105.5, ENST00000672818.3 )
MUTYH p.Arg516Gln (p.R516Q), ENSG00000288208 c.*215G>A ( ENST00000354383.10, ENST00000355498.6, ENST00000372098.7, ENST00000372104.5, ENST00000372110.7, ENST00000372115.7, ENST00000412971.6, ENST00000448481.5, ENST00000456914.7, ENST00000483127.2, ENST00000488731.6, ENST00000528013.6, ENST00000529892.6, ENST00000529984.5, ENST00000531105.5, ENST00000672314.2, ENST00000672818.3, ENST00000710952.2, ENST00000713750.1, ENST00000713751.1 )
Associated Disease
familial adenomatous polyposis 2
Source Database
ClinVar
Description
NM_001048174.2(MUTYH):c.1472G>A (p.Arg491Gln) AND Familial adenomatous polyposis 2
ClinVar Allele ID
133298
ClinVar RefSeq Alternation Syntax
NM_001293196.2:c.1196G>A
ClinVar RefSeq Alternation Syntax
NM_001293195.2:c.1472G>A
ClinVar RefSeq Alternation Syntax
NM_012222.3:c.1547G>A
ClinVar RefSeq Alternation Syntax
NM_001293192.2:c.1196G>A
ClinVar RefSeq Alternation Syntax
NM_001350650.2:c.1127G>A
ClinVar RefSeq Alternation Syntax
NM_001048171.2:c.1472G>A
ClinVar RefSeq Alternation Syntax
NM_001048173.2:c.1472G>A
ClinVar RefSeq Alternation Syntax
NM_001293191.2:c.1505G>A
ClinVar RefSeq Alternation Syntax
NM_001048172.2:c.1475G>A
ClinVar RefSeq Alternation Syntax
NM_001350651.2:c.1127G>A
ClinVar RefSeq Alternation Syntax
NM_001128425.2:c.1556G>A
ClinVar RefSeq Alternation Syntax
NR_146882.2:n.1880G>A
ClinVar RefSeq Alternation Syntax
NM_001048174.2:c.1472G>A
ClinVar RefSeq Alternation Syntax
NR_146883.2:n.1729G>A
ClinVar RefSeq Alternation Syntax
NM_001293190.2:c.1517G>A
Clinical Significance Description
Uncertain significance
Clinical Significance Last Update
2024-01-08
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000123146
ClinVar Disease
Familial adenomatous polyposis 2
Observed Origin Sample
germline
Observed Origin Sample
unknown
Drugs