Annotation Detail

Information
Associated Genes
MTFMT
Associated Variants
MTFMT p.Gln25Ter (p.Q25*) ( ENST00000220058.9 )
MTFMT p.Gln25Ter (p.Q25*) ( ENST00000220058.9 )
Associated Disease
Combined oxidative phosphorylation defect type 15
Source Database
ClinVar
Description
NM_139242.4(MTFMT):c.73C>T (p.Gln25Ter) AND Combined oxidative phosphorylation defect type 15
Observed Origin Sample
germline
Pubmed
24461907
ClinVar Allele ID
137062
ClinVar RefSeq Alternation Syntax
NM_139242.4:c.73C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2014-03-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000119837
ClinVar Disease
Combined oxidative phosphorylation defect type 15
Drugs