Annotation Detail

Information
Associated Genes
VHL
Associated Variants
VHL p.Pro81Ser (p.P81S) ( ENST00000256474.3, ENST00000345392.3, ENST00000696143.2, ENST00000696153.1, ENST00000713811.1, ENST00000713812.1, ENST00000713815.1, ENST00000713982.1 )
VHL p.Pro81Ser (p.P81S) ( ENST00000256474.3, ENST00000345392.3, ENST00000696143.2, ENST00000696153.1, ENST00000713811.1, ENST00000713812.1, ENST00000713815.1, ENST00000713982.1 )
Associated Disease
Hereditary cancer-predisposing syndrome
Source Database
ClinVar
Description
NM_000551.4(VHL):c.241C>T (p.Pro81Ser) AND Hereditary cancer-predisposing syndrome
ClinVar Allele ID
17272
ClinVar RefSeq Alternation Syntax
NM_001354723.2:c.241C>T
ClinVar RefSeq Alternation Syntax
NM_198156.3:c.241C>T
ClinVar RefSeq Alternation Syntax
NM_000551.4:c.241C>T
Clinical Significance Description
Conflicting interpretations of pathogenicity
Clinical Significance Last Update
2022-01-25
Clinical Significance Review Status
criteria provided, conflicting interpretations
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000115744
ClinVar Disease
Hereditary cancer-predisposing syndrome
Observed Origin Sample
germline
Drugs