Annotation Detail

Information
Associated Genes
LZTR1
Associated Variants
LZTR1 p.Thr783ArgfsTer5 (p.T783Rfs*5) ( ENST00000646124.2, ENST00000700578.1 )
LZTR1 p.Thr783ArgfsTer5 (p.T783Rfs*5) ( ENST00000646124.2, ENST00000700578.1 )
Associated Disease
schwannomatosis 2
Source Database
ClinVar
Description
NM_006767.4(LZTR1):c.2348_2351del (p.Thr783fs) AND Schwannomatosis 2
ClinVar Allele ID
106802
ClinVar RefSeq Alternation Syntax
NM_006767.4:c.2348_2351del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2014-02-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000087295
ClinVar Disease
Schwannomatosis 2
Observed Origin Sample
unknown
Pubmed
24362817
Drugs