Annotation Detail

Information
Associated Genes
LZTR1
Associated Variants
LZTR1 p.Arg688Cys (p.R688C) ( ENST00000646124.2, ENST00000700578.1 )
LZTR1 p.Arg688Cys (p.R688C) ( ENST00000646124.2, ENST00000700578.1 )
Associated Disease
schwannomatosis 2
Source Database
ClinVar
Description
NM_006767.4(LZTR1):c.2062C>T (p.Arg688Cys) AND Schwannomatosis 2
ClinVar Allele ID
106801
ClinVar RefSeq Alternation Syntax
NM_006767.4:c.2062C>T
Clinical Significance Description
Conflicting interpretations of pathogenicity
Clinical Significance Last Update
2023-06-07
Clinical Significance Review Status
criteria provided, conflicting interpretations
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000087294
ClinVar Disease
Schwannomatosis 2
Observed Origin Sample
germline
Observed Origin Sample
unknown
Pubmed
24362817
Pubmed
30442762
Drugs