Annotation Detail

Information
Associated Genes
GLB1
Associated Variants
GLB1 p.Phe308Leu (p.F308L) ( ENST00000307363.10, ENST00000307377.12, ENST00000399402.7 )
GLB1 p.Phe308Leu (p.F308L) ( ENST00000307363.10, ENST00000307377.12, ENST00000399402.7 )
Associated Disease
Infantile GM1 gangliosidosis
Source Database
ClinVar
Description
NM_000404.4(GLB1):c.922T>C (p.Phe308Leu) AND Infantile GM1 gangliosidosis
ClinVar Allele ID
106592
ClinVar RefSeq Alternation Syntax
NM_001135602.3:c.529T>C
ClinVar RefSeq Alternation Syntax
NM_001393580.1:c.922T>C
ClinVar RefSeq Alternation Syntax
NM_001317040.2:c.1066T>C
ClinVar RefSeq Alternation Syntax
NM_000404.4:c.922T>C
ClinVar RefSeq Alternation Syntax
NM_001079811.3:c.832T>C
Clinical Significance Description
Pathogenic
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000087093
ClinVar Disease
Infantile GM1 gangliosidosis
Observed Origin Sample
inherited
Drugs