Annotation Detail

Information
Associated Genes
IDUA
Associated Variants
IDUA p.Gly409Arg (p.G409R) ( ENST00000247933.9, ENST00000514224.2 )
IDUA p.Gly409Arg (p.G409R) ( ENST00000247933.9, ENST00000514224.2 )
Associated Disease
not specified
Source Database
ClinVar
Description
NM_000203.5(IDUA):c.1225G>C (p.Gly409Arg) AND not specified
ClinVar Allele ID
26950
ClinVar RefSeq Alternation Syntax
NM_000203.5:c.1225G>C
ClinVar RefSeq Alternation Syntax
NM_001363576.1:c.829G>C
ClinVar RefSeq Alternation Syntax
NR_110313.1:n.1313G>C
Clinical Significance Description
Conflicting interpretations of pathogenicity
Clinical Significance Last Update
2022-03-07
Clinical Significance Review Status
criteria provided, conflicting interpretations
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000078375
ClinVar Disease
not specified
Observed Origin Sample
germline
Observed Origin Sample
unknown
Drugs