Annotation Detail

Information
Associated Genes
FAT4
Associated Variants
FAT4 p.Ser4840LeufsTer3 (p.S4840Lfs*3) ( ENST00000335110.5, ENST00000394329.9, ENST00000674496.2 )
FAT4 p.Ser4840LeufsTer3 (p.S4840Lfs*3) ( ENST00000335110.5, ENST00000394329.9, ENST00000674496.2 )
Associated Disease
Van Maldergem syndrome 2
Source Database
ClinVar
Description
NM_001291303.3(FAT4):c.14518_14519del (p.Ser4840fs) AND Van Maldergem syndrome 2
ClinVar Allele ID
94562
ClinVar RefSeq Alternation Syntax
NM_024582.6:c.14512_14513del
ClinVar RefSeq Alternation Syntax
NM_001291285.3:c.14515_14516del
ClinVar RefSeq Alternation Syntax
NM_001291303.3:c.14518_14519del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2013-11-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000074492
ClinVar Disease
Van Maldergem syndrome 2
Observed Origin Sample
germline
Pubmed
22469822
Pubmed
24056717
Drugs