Annotation Detail

Information
Associated Genes
PRNP
Associated Variants
PRNP p.Tyr145Ter (p.Y145*) ( ENST00000379440.9, ENST00000424424.2, ENST00000430350.2, ENST00000457586.2 )
PRNP p.Tyr145Ter (p.Y145*) ( ENST00000379440.9, ENST00000424424.2, ENST00000430350.2, ENST00000457586.2 )
Associated Disease
CEREBRAL AMYLOID ANGIOPATHY, PRNP-RELATED
Source Database
ClinVar
Description
NM_000311.5(PRNP):c.435T>G (p.Tyr145Ter) AND CEREBRAL AMYLOID ANGIOPATHY, PRNP-RELATED
Observed Origin Sample
germline
ClinVar Allele ID
33999
ClinVar RefSeq Alternation Syntax
NM_000311.5:c.435T>G
ClinVar RefSeq Alternation Syntax
NM_001080122.3:c.435T>G
ClinVar RefSeq Alternation Syntax
NM_183079.4:c.435T>G
ClinVar RefSeq Alternation Syntax
NM_001080123.3:c.435T>G
ClinVar RefSeq Alternation Syntax
NM_001271561.3:c.*124T>G
ClinVar RefSeq Alternation Syntax
NM_001080121.3:c.435T>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1996-01-23
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000074469
ClinVar Disease
CEREBRAL AMYLOID ANGIOPATHY, PRNP-RELATED
Pubmed
8570627
Drugs