Annotation Detail

Information
Associated Genes
G6PD
Associated Variants
G6PD p.Asn363Lys (p.N363K) ( ENST00000369620.6, ENST00000393562.10, ENST00000393564.7, ENST00000439227.6, ENST00000696420.1, ENST00000696421.1, ENST00000696429.1, ENST00000696430.1 )
G6PD p.Asn363Lys (p.N363K) ( ENST00000369620.6, ENST00000393562.10, ENST00000393564.7, ENST00000439227.6, ENST00000696420.1, ENST00000696421.1, ENST00000696429.1, ENST00000696430.1 )
Associated Disease
Anemia, nonspherocytic hemolytic, due to G6PD deficiency
Source Database
ClinVar
Description
NM_000402.4(G6PD):c.1179C>A (p.Asn393Lys) AND Anemia, nonspherocytic hemolytic, due to G6PD deficiency
ClinVar Allele ID
25429
ClinVar RefSeq Alternation Syntax
NM_001042351.3:c.1089C>A
ClinVar RefSeq Alternation Syntax
NM_000402.4:c.1179C>A
ClinVar RefSeq Alternation Syntax
NM_001360016.2:c.1089C>A
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2022-08-12
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000066262
ClinVar Disease
Anemia, nonspherocytic hemolytic, due to G6PD deficiency
Observed Origin Sample
germline
Observed Origin Sample
unknown
Pubmed
1978554
Drugs