Annotation Detail

Information
Associated Genes
KCNH2
Associated Variants
KCNH2 p.Thr65Pro (p.T65P) ( ENST00000262186.10, ENST00000713710.1 )
KCNH2 p.Thr65Pro (p.T65P) ( ENST00000262186.10, ENST00000713710.1 )
Associated Disease
Congenital long QT syndrome
Source Database
ClinVar
Description
NM_000238.4(KCNH2):c.193A>C (p.Thr65Pro) AND Congenital long QT syndrome
ClinVar Allele ID
29473
ClinVar RefSeq Alternation Syntax
NM_000238.4:c.193A>C
ClinVar RefSeq Alternation Syntax
NM_001406755.1:c.16A>C
ClinVar RefSeq Alternation Syntax
NM_172056.3:c.193A>C
Clinical Significance Description
not provided
Clinical Significance Review Status
no assertion provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000058063
ClinVar Disease
Congenital long QT syndrome
Observed Origin Sample
germline
Drugs