Annotation Detail

Information
Associated Genes
MYH7
Associated Variants
MYH7 p.Tyr283Asp (p.Y283D) ( ENST00000355349.4, ENST00000713768.1, ENST00000713769.1 )
MYH7 p.Tyr283Asp (p.Y283D) ( ENST00000355349.4, ENST00000713768.1, ENST00000713769.1 )
Associated Disease
Left ventricular noncompaction 5
Source Database
ClinVar
Description
NM_000257.4(MYH7):c.847T>G (p.Tyr283Asp) AND Left ventricular noncompaction 5
ClinVar Allele ID
76983
ClinVar RefSeq Alternation Syntax
NM_000257.4:c.847T>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2011-02-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000056316
ClinVar Disease
Left ventricular noncompaction 5
Observed Origin Sample
germline
Pubmed
21127202
Drugs