Annotation Detail

Information
Associated Genes
CYP21A2 LOC106780800
Associated Variants
CYP21A2 p.Val282Leu (p.V282L) ( ENST00000435122.3, ENST00000644719.2 )
CYP21A2 p.Val282Leu (p.V282L) ( ENST00000435122.3, ENST00000644719.2 )
Associated Disease
Classic congenital adrenal hyperplasia due to 21-hydroxylase deficiency
Source Database
ClinVar
Description
NM_000500.9(CYP21A2):c.844G>C (p.Val282Leu) AND Classic congenital adrenal hyperplasia due to 21-hydroxylase deficiency
ClinVar Allele ID
76518
ClinVar RefSeq Alternation Syntax
NM_001128590.4:c.754G>C
ClinVar RefSeq Alternation Syntax
NM_000500.9:c.844G>C
ClinVar RefSeq Alternation Syntax
NM_001368144.2:c.439G>C
ClinVar RefSeq Alternation Syntax
NM_001368143.2:c.439G>C
Clinical Significance Description
not provided
Clinical Significance Review Status
no assertion provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000055820
ClinVar Disease
Classic congenital adrenal hyperplasia due to 21-hydroxylase deficiency
Observed Origin Sample
unknown
Drugs